A 3-month-old infant presents with hepatomegaly, hypoglycemia, and lactic acidosis. Physical examination reveals a 'doll-like' face and renomegaly. Muscle strength is normal. Which enzyme deficiency is most likely responsible for this condition?
✓ Correct Answer: Option B
This clinical presentation is classic for Von Gierke disease (Type I Glycogen Storage Disease), caused by a deficiency in glucose-6-phosphatase, which impairs glucose release from the liver and kidneys.